Restrictive Lung Disease USMLE Step 1 Practice Question
A 41-year-old aerospace engineer presents with 6 months of progressive dyspnea, fatigue, and nonproductive cough. Vital signs show BP 128/82, HR 102, RR 22, SpO2 88% on room air. Chest CT reveals diffuse interstitial infiltrates and bilateral hilar lymphadenopathy. Serum ACE level is elevated at 68 U/L. Lung biopsy demonstrates noncaseating granulomas. Tuberculin skin test is negative. Which of the following is the most likely diagnosis?
Answer choices
- ATuberculosis
- BIdiopathic pulmonary fibrosis
- CSarcoidosis
- DHypersensitivity pneumonitis
- EBerylliosisCorrect answer
- FLangerhans cell histiocytosis (pulmonary)
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